[Stiff skin syndrome in a pediatric patient: a therapeutic challenge. Clinical case]

Abstract

Abstract in English, Spanish Stiff skin syndrome is a chronic, rare sclerosing disorder that occurs in childhood, characterized by progressive induration of the skin that can cause thoracic restrictions and respiratory distress, limitations in joint mobility and gait difficulties, with significant deterioration of the quality of life. Because their therapeutic options are scarce and ineffective it is essential to start an early physical therapy to prevent these complications and to continue studying this condition to be able to offer patients more and better treatments. We present the case of a 9-year-old patient with indurated skin syndrome and its therapeutic challenge.

Keywords: losartan; skin and connective tissue diseases; stiff skin syndrome.

Sociedad Argentina de Pediatría.

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